DeCS Server - List Exact Term

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DeCS

Descriptor English:

Multiple System Atrophy

Descriptor Spanish:

Atrofia de Múltiples Sistemas

Descriptor Portuguese:

Atrofia de Múltiplos Sistemas

Tree Number:

Definition English:

A syndrome complex composed of three conditions which represent clinical variants of the same disease process: STRIATONIGRAL DEGENERATION; SHY-DRAGER SYNDROME; and the sporadic form of OLIVOPONTOCEREBELLAR ATROPHIES. Clinical features include autonomic, cerebellar, and basal ganglia dysfunction. Pathologic examination reveals atrophy of the basal ganglia, cerebellum, pons, and medulla, with prominent loss of autonomic neurons in the brain stem and spinal cord. (From Adams et al., Principles of Neurology, 6th ed, p1076; Baillieres Clin Neurol 1997 Apr;6(1):187-204; Med Clin North Am 1999 Mar;83(2):381-92)

Indexing Annotation English:

a specific neurodegenerative syndrome complex; not for atrophy in other systems

See Related English:

History Note English:

1998

Allowable Qualifiers English:

Record Number:

33352

Unique Identifier:

D019578

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